Aplasia cutis congenita of the scalp: therapeutic modalities.
@article{Shivakumar2006AplasiaCC,
title={Aplasia cutis congenita of the scalp: therapeutic modalities.},
author={Sudeep Shivakumar and Srinivas Dwarakanath and G R Swaroop and Neelam K Venkataramana},
journal={Neurology India},
year={2006},
volume={54 3},
pages={
312-3
}
}Agenesis of scalp is an uncommon but well-recognized clinical entity. Congenital scalp and skull defects can be either obvious or occult; over 300 cases have been reported in literature. Aplasia cutis congenita (ACC) is recognized as a heterogeneous disorder, all characterized by focal absence of the epidermis, dermis and sometimes the calvarium and/or dura. We present a case of ACC in an infant whose mother was exposed to a teratogenic drug (Methimazole--an antithyroid drug) during pregnancy…
20 Citations
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In patients with large scalp and skull defects, there is increased risk of infection and bleeding along with increased mortality and therefore prompt and effective management is advised, and decision between conservative and surgical management must be individualized according to lesion size and location.
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In patients with large scalp and skull defects, there is increased risk of infection and bleeding along with increased mortality and therefore prompt and effective management is advised, and decision between conservative and surgical management must be individualized according to lesion size and location.
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This study reviews indications and modalities for treatment of this rare congenital anomaly and concludes that using conservative and surgical modalities, one can achieve complete closure of the defect, thus avoiding risks of infection, hemorrhage, and further trauma.
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Histopathological evaluation of specimens obtained from patients operated on for ACC revealed the characteristics of the scar, and aesthetic results of surgical management were assessed as good in the presented cases.
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Aplasia cutis congenita is a congenital defect consisting of a circumscribed absence of skin that usually involves the scalp and several teratogenic agents such as methimazole have been involved.
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The authors emphasize the role of emergency split-thickness skin grafting in the treatment of large aplasia cutis congenita or ones with large veins or sagittal sinus exposure and offer a treatment guideline.
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- Accepted on 22-02-2006 Neurology India | September 2006 | Vol
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