Aortic Involvement in Pediatric Marfan syndrome: A Review

  title={Aortic Involvement in Pediatric Marfan syndrome: A Review},
  author={Omonigho Ekhomu and Zahra J. Naheed},
  journal={Pediatric Cardiology},
Outlining specific protocols for the management of pediatric patients with Marfan syndrome has been challenging. This is mostly due to a dearth of clinical studies performed in pediatric patients. In Marfan syndrome, the major sources of morbidity and mortality relate to the cardiovascular system. In this review, we focus on aortic involvement seen in pediatric patients with Marfan syndrome, ranging from aortic dilatation to aortic rupture and heart failure. We discuss the histological… CONTINUE READING