Anxiety, Fears, and Phobias in Persons With Williams Syndrome

@article{Dykens2003AnxietyFA,
  title={Anxiety, Fears, and Phobias in Persons With Williams Syndrome},
  author={E. Dykens},
  journal={Developmental Neuropsychology},
  year={2003},
  volume={23},
  pages={291 - 316}
}
  • E. Dykens
  • Published 2003
  • Psychology, Medicine
  • Developmental Neuropsychology
Although much research has focused on the cognitive-linguistic profile associated with Williams syndrome, studies have yet to follow up on preliminary observations suggesting increased anxiety and fears in persons with this disorder. To this aim, Study 1 compared fears in 120 participants with Williams syndrome to 70 appropriately matched persons with mental retardation of mixed etiologies. Study 2 assessed differences in parent versus child reports of fears in 36 Williams syndrome and 24… Expand
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It is suggested that children with ASD exhibit a distinct profile of fear and anxiety compared to other mental age and chronologically age-matched children, and these fears are related to the symptoms associated with ASD. Expand
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A hypothesis that fears and anxiety could be associated with hyperacusis in the WS population is supported and a hypothesis that musicality could serve as a protective factor and prevent anxiety, received no or very limited support. Expand
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TLDR
The adults with WS provided reliable information regarding their mental health, thus providing further evidence that anxiety is part of the behavioural phenotype of the syndrome. Expand
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TLDR
Severity of anxiety was correlated with a greater degree of social dysfunction as measured by the SRS in this group and the profile of social skills for the two groups differed in their social abilities. Expand
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There was a significant relation between executive functioning and anxiety such that the presence of an anxiety diagnosis was associated with increased scores on behavioral regulation, indicative of increased difficulty with inhibitory control of affect and behavior. Expand
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