Anesthetic problems in Rubinstein-Taybi syndrome.

@article{Stirt1981AnestheticPI,
  title={Anesthetic problems in Rubinstein-Taybi syndrome.},
  author={Joseph A. Stirt},
  journal={Anesthesia and analgesia},
  year={1981},
  volume={60 7},
  pages={
          534-6
        }
}
  • J. Stirt
  • Published 1 July 1981
  • Medicine
  • Anesthesia and analgesia
Rubinstein-Taybi syndrome is a congenital anomaly characterized b y broad thumbs and first toes, facial abnormalities, and mental retardation (1, 2). There are no published reports of anesthetic-related problems in patients with this syndrome. I describe here the rather eventful course of three separate anesthetics administered over a period of 12 years to a single patient with Rubinstein-Taybi syndrome. 
Anesthetic Implications in Rubinstein-Taybi Syndrome
TLDR
A 5-year-old boy with RTS that required anesthetic care for an adenotonsillectomy is presented and the perioperative considerations of these patients are discussed. Expand
Anaesthesia in an infant with Rubinstein‐Taybi syndrome
TLDR
The anaesthetic management of a 5‐month‐old Chinese infant with Rubinstein‐Taybi syndrome requiring bilateral inguinal hernia repairs is described, and general anaesthesia combined with caudal block was successfully used. Expand
Rubinstein-Taybi syndrome in The Netherlands.
TLDR
Patients with Rubinstein-Taybi syndrome living in The Netherlands had broad halluces, but only 39 patients had broad thumbs, probably due to abnormal anatomy in the craniofacial region. Expand
Anaesthetic Management of Children with Rubinstein-Taybi Syndrome.
TLDR
The anaesthesia management of a child with RTS who underwent right endoscopic dacryocystorhinostomy was discussed, including the possibilities of difficult airway, aspiration pneumonia and cardiovascular dysfunction during anaesthesia. Expand
Anesthetic management of children with Rubinstein-Taybi syndrome--case reports.
TLDR
This case series examines the cases of three pediatric patients with Rubinstein-Taybi Syndrome who presented to the Children's Hospital of Michigan for different surgeries and adjusted techniques using information from preceding cases to avoid complications in the following encounter. Expand
ANESTHETIC MANAGEMENT OF CHILDREN WITH RUBINSTEIN-TAYBI SYNDROME-Case Reports
A limited number of cases of anesthetic management of Rubinstein-Taybi Syndrome (RTS) have been reported since this syndrome was first diagnosed in 1963. After some well-publicized complicationsExpand
Anesthetic management for thoracic surgery in Rubinstein-Taybi syndrome.
TLDR
The anesthetic management in a RTS patient undergoing emergent thoracic surgery due to oesophageal perforation and mediastinitis was reported to be successfully and one-lung ventilation was performed successfully. Expand
Broad thumb-hallux (Rubinstein-Taybi) syndrome 1957-1988.
  • J. Rubinstein
  • Medicine, Biology
  • American journal of medical genetics. Supplement
  • 1990
TLDR
The diagnosis was established in most cases by confirming the concurrence of the constellation of major diagnostic criteria, including broad short terminal phalanges of the thumbs and halluces with or without angulation deformity. Expand
Rubinstein-Taybi syndrome: a natural history study.
TLDR
Individuals with Rubinstein-Taybi syndrome were found to have particular difficulty with expressive speech skills, and indexes for maladaptive behavior were calculated showing that approximately 10% of patients had significant behavior problems. Expand
Rubinstein‐Taybi syndrome medical guidelines
TLDR
This is a first attempt at medical guidelines for individuals with RTS in the United States, and recommendations for specific surveillance and interventions are made to guide those clinicians caring for Individuals with Rubinstein‐Taybi Syndrome. Expand
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In 1963 Rubinstein and Taybi published a report on seven children with mental retardation, abnormal facial features and broad thumbs and great toes. The following year Coffin (1964) described sixExpand
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