Analysis of the Posterior Fossa in Children with the Chiari 0 Malformation

@article{Tubbs2001AnalysisOT,
  title={Analysis of the Posterior Fossa in Children with the Chiari 0 Malformation},
  author={R. Shane Tubbs and Scott W. Elton and Paul A. Grabb and Stephen E. Dockery and Alfred A. Bartolucci and Walter Jerry Oakes},
  journal={Neurosurgery},
  year={2001},
  volume={48},
  pages={1050-1055}
}
OBJECTIVE We previously reported the resolution of syringohydromyelia without cerebellar tonsillar ectopia in five patients after posterior fossa decompression of the so-called Chiari 0 malformation. A sixth patient is described. In this study, the anatomy of the posterior fossa is analyzed using radiological imaging, enabling features of the posterior fossa in this uncommon subgroup of children to be characterized. METHODS Multiple measurements were made on magnetic resonance imaging studies… 
Posterior fossa dimension and volume estimates in pediatric patients with Chiari I malformations
TLDR
Mean PFV values were found to be smaller in pediatric CMI patients than control patients; this complements earlier studies in adults and supports the present theory concerning the pathophysiological mechanism of CMI.
Epidemiology of Chiari I Malformation
TLDR
More rigorous measurements of the prevalence and incidence of Chiari I malformation would result from prospective epidemiologic studies of large populations designed for this purpose than from retrospective queries of the databases of private and governmental healthcare organizations.
Dimensions of the posterior fossa in patients symptomatic for Chiari I malformation but without cerebellar tonsillar descent
TLDR
Preliminary morphologic data suggests that a subgroup of patients exists with tonsillar descent less than 3 mm below the foramen magnum but with congenitally hypoplastic posterior fossa causing symptomatology consistent with CMI.
Chiari I Malformation in the Adult
TLDR
Treatment today consists of suboccipital decompression to reestablish optimal CSF flow from the fourth ventricle, recreate a subtonsillar cistern, and relieve brainstem compression to improve surgical management of Chiari malformation.
Pediatric Chiari malformation Type 0: a 12-year institutional experience.
TLDR
It is stressed that careful patient selection is critical when diagnosing CM-0, without an obvious CM-I, other etiologies of a spinal syrinx must be conclusively ruled out, and one reasonably expects to ameliorate the clinical course of these patients via posterior fossa decompression.
Chiari malformation and syringomyelia.
TLDR
Primary spinal syringomyelia (PSS) can be caused by traumatic, infectious, degenerative, and other etiologies that cause at least a partialCSF flow obstruction in the spinal subarachnoid space, and the main goal of PSS surgery is to reestablish CSF flow across the area of obstruction.
Critical analysis of the Chiari malformation Type I found in children with lipomyelomeningocele.
TLDR
The incidence of CM-I in patients with lipomyelomeningocele appears to be significantly greater than that of the general population and the association rate is too high for the finding to be a chance occurrence.
A critical analysis of the Chiari 1.5 malformation.
TLDR
No single sign or symptom was found to be peculiar to the Chiari 1.5 malformation, although all patients in whom this diagnosis was established had undergone a posterior fossa decompressive surgery, and Neurosurgeons may wish to consider that many patients may not respond as well to posterior Fossa decompression surgery especially if syringomyelia is present.
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TLDR
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TLDR
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