Anaesthetic management of a patient with Charcot-Marie-Tooth disease for staged diaphragmatic plication.

@article{Pasha2013AnaestheticMO,
  title={Anaesthetic management of a patient with Charcot-Marie-Tooth disease for staged diaphragmatic plication.},
  author={Tina Pasha and A Knowles},
  journal={British journal of anaesthesia},
  year={2013},
  volume={110 6},
  pages={
          1061-3
        }
}
Editor—With great interest, we have read the article by Pasha and Knowles. We found it to be a very interesting article as it offers more information on these patients’ anaesthetic management. The authors describe two types of anaesthesia in the same patient and used vecuronium in the first. Under anaesthesia, they describe a possible residual effect with vecuronium. As they mention in their article, there is considerable dispute about the use of neuromuscular blocking agents in these patients… 

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References

SHOWING 1-10 OF 32 REFERENCES
[Anesthetic management for pancreaticoduodenectomy in a patient with Charcot-Marie-Tooth disease and liver cirrhosis].
TLDR
It is suggested that monitoring neuromuscular function may be necessary to detect subtle residual neuromUScular blockade when rocuronium is used in a patient with CMTD and liver dysfunction.
Anaesthesia for charcot-marie-tooth disease: a review of 86 cases
  • J. Antognini
  • Medicine
    Canadian journal of anaesthesia = Journal canadien d'anesthesie
  • 1992
TLDR
This survey supports the safe use of succinylcholine and MH triggering agents in Charcot-Marie-Tooth disease, a condition characterized by chronic muscular denervation, without untoward effects.
Response to atracurium and mivacurium in a patient with Charcot-Marie-Tooth disease
TLDR
There was no evidence of prolonged response to atracurium and mivacurium in a patient with CMTD during nitrous oxide-oxygen-alfentanil-propofol anaesthesia.
Vecuronium neuromuscular block in a patient with Charcot-Marie-Tooth syndrome.
  • A. Baraka
  • Medicine, Psychology
    Anesthesia and analgesia
  • 1997
TLDR
The present case report investigates the neuromuscular block of vecuronium in an adolescent with CMT syndrome and introduces concerns regarding altered response to anesthetics such as thiopental and nondepolarizing muscle relaxants.
Epidural analgesia for labour in a patient with Charcot-Marie-Tooth disease
  • T. Scull, S. Weeks
  • Medicine
    Canadian journal of anaesthesia = Journal canadien d'anesthesie
  • 1996
TLDR
Epidural analgesia, after thorough discussion with the patient, may be offered to parturients with CMT and this disease, together with the current literature on the provision of epidural and general anaesthesia in this disease are reviewed.
Intrathecal drug spread.
TLDR
This review focuses in particular on work published in the last decade in trying to provide guidance on making spinal anaesthesia as predictable as possible.
Long term results of diaphragmatic plication for unilateral diaphragm paralysis.
Diaphragm plication in adult patients with diaphragm paralysis leads to long-term improvement of pulmonary function and level of dyspnea.
  • M. Versteegh, J. Braun, R. Dion
  • Medicine
    European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery
  • 2007
Malignant hyperthermia during sevoflurane administration.
TLDR
A 20-yr-old woman with a history of Charcot-Marie-Tooth disease (Type II) and underwent an osteotomy of the right calcaneum under general anesthesia without problems, although the anesthetics used are unknown.
...
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