An unusually presenting case of sCJD--the VV1 subtype.

  title={An unusually presenting case of sCJD--the VV1 subtype.},
  author={Kaloyan S Tanev and Mimi Yilma},
  journal={Clinical neurology and neurosurgery},
  volume={111 3},
Creutzfeldt-Jakob disease (CJD) is a rapidly progressive neurodegenerative disease caused by prions. Typically CJD presents with a triad of rapidly progressive dementia, abnormal movements (e.g., myoclonus) and electroencephalographic (EEG) changes. Recently, CJD has been subdivided into subtypes based on host genetic polymorphisms and the characteristics of the pathological prion protein. Different subtypes likely have different clinical and laboratory presentations. We describe a case of… CONTINUE READING