Submitted: 06‐05‐2015 Revised: 22‐05‐2015 Published: 01‐07‐2015 Inflammatory myofibroblastic tumor (IMT) of the bladder is an uncommon benign tumor of the urinary bladder, which is of unknown neoplastic potential, characterized by spindle cell proliferation with characteristic fibro inflammatory and pseudosarcomatous appearance of mesenchymal origin. Myofibroblastic tumor, is also known as inflammatory pseudotumor or pseudosarcoma. Bladder location is very uncommon. We report a case of a young girl who presented with acute kidney injury due to obstructive uropathy. On evaluation found to have Inflammatory myofibroblastic tumor at the base of the urinary bladder, which gradually improved with hemodialysis and successive urological interventions.