Aldolase B and fructose intolerance

@article{Cox1994AldolaseBA,
  title={Aldolase B and fructose intolerance},
  author={T. Cox},
  journal={The FASEB Journal},
  year={1994},
  volume={8},
  pages={62 - 71}
}
  • T. Cox
  • Published 1994
  • Biology, Medicine
  • The FASEB Journal
Hereditary fructose intolerance is an autosomal recessive disorder that illustrates vividly the interplay between heredity and environment in the genesis of human nutritional disease. Genetically determined defects of an isozyme of fructose bisphosphate aldolase (aldolase B, which is specialized for the metabolic assimilation of dietary sugars) predispose to this widely distributed condition. Ingestion of fructose, sorbitol, or sucrose induces abdominal pain, vomiting, and metabolic… Expand
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