Adult onset of multisystem Langerhans cell histiocytosis with skin and lymph node involvement

  title={Adult onset of multisystem Langerhans cell histiocytosis with skin and lymph node involvement},
  author={Izabela Błażewicz and W. Biernat and A. Kowalczyk and W. Barańska-Rybak and R. Nowicki and Marta Stawczyk-Macieja and M. Sokołowska-Wojdyło},
  journal={Advances in Dermatology and Allergology/Postȩpy Dermatologii i Alergologii},
  pages={225 - 228}
  • Izabela Błażewicz, W. Biernat, +4 authors M. Sokołowska-Wojdyło
  • Published 2015
  • Medicine
  • Advances in Dermatology and Allergology/Postȩpy Dermatologii i Alergologii
  • Langerhans cell histiocytosis (LCH) is a rare disorder characterized by clonal proliferation of dendritic cells, which comprises a wide range of clinical presentations. The term LCH is used to include a spectrum of disorders previously termed: histiocytosis X, eosinophilic granuloma, Hand-Schuller-Christian disease, Letterer-Siwe disease and Hashimoto-Pritzker disease. The etiology of the lesion is still elusive, and the question of whether LCH is a reactive or neoplastic disorder remains… CONTINUE READING
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