Salivary gland neoplasm of the head and neck region are consisting of 1-5% of the total malignancies. Adenoid cystic carcinoma (ACC) is the one of the most common malignancy of the salivary gland. It is considered as one of the an intermediate grade of salivary gland neoplasms. ACC is characterized by slow growth, which causes extensive invasion and aggressive ability for early metastastic deposits, the factors which makes the behavior of the neoplasm aggressive. Here with, reporting a case of adenoid cystic carcinoma involving the left side of the hard palate, along with its review of literature.