Acute encephalopathy as a primary manifestation of haemophagocytic lymphohistiocytosis.

Abstract

Haemophagocytic lymphohistiocytosis (HLH) is characterized anatomically by an infiltration of multiple tissues with lymphocytes and haemophagocytic histiocytes. First symptoms are usually hepatosplenomegaly, pancytopenia, and intractable fever. Up to 73% of those with HLH develop CNS involvement during the disease course. The peculiarity of the two patients… (More)

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Cite this paper

@article{Kieslich2001AcuteEA, title={Acute encephalopathy as a primary manifestation of haemophagocytic lymphohistiocytosis.}, author={Moritz Kieslich and Maurizio Vecchi and Pablo Hern{\'a}iz Driever and Anna Maria Laverda and Dirk Schwabe and G. W. Jacobi}, journal={Developmental medicine and child neurology}, year={2001}, volume={43 8}, pages={555-8} }