A arteries in Marfan syndrome: CT coronary angiography
- I Vasies
Marfan syndrome (MS) is an inherited connective tissue disorder that is responsible for a variety of abnormalities of the cardiovascular system. The prevalence of abnormal aortic origin of coronary arteries in the general population ranges between 0.6 and 1.3% on angiography studies  and reaches 1.96% on computed tomography coronary angiography (CTCA) [2—4]. Interarterial course is rare, but represents a risk factor of sudden death, especially on exercise or after exercise. The association between MS and abnormal aortic origin of coronary arteries was scarcely reported in the literature . We describe the imaging presentation of abnormal origin and interarterial course of coronary arteries in a patient with MS on CTCA and emphasize the role of this technique for the depiction of this abnormality.