Abnormal origin and interarterial course of coronary arteries in Marfan syndrome: CT coronary angiography features.

Abstract

Marfan syndrome (MS) is an inherited connective tissue disorder that is responsible for a variety of abnormalities of the cardiovascular system. The prevalence of abnormal aortic origin of coronary arteries in the general population ranges between 0.6 and 1.3% on angiography studies [1] and reaches 1.96% on computed tomography coronary angiography (CTCA) [2—4]. Interarterial course is rare, but represents a risk factor of sudden death, especially on exercise or after exercise. The association between MS and abnormal aortic origin of coronary arteries was scarcely reported in the literature [5]. We describe the imaging presentation of abnormal origin and interarterial course of coronary arteries in a patient with MS on CTCA and emphasize the role of this technique for the depiction of this abnormality.

DOI: 10.1016/j.diii.2015.11.006

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Cite this paper

@article{Vasies2016AbnormalOA, title={Abnormal origin and interarterial course of coronary arteries in Marfan syndrome: CT coronary angiography features.}, author={I Vasies and Benjamin Dubourg and Marta Lempicki and Fabien Doguet and Jean-Nicolas Dacher}, journal={Diagnostic and interventional imaging}, year={2016}, volume={97 6}, pages={691-3} }