A variant of Cenani-Lenz syndactyly (CLS): review of the literature and attempt of classification.

@article{Harpf2005AVO,
  title={A variant of Cenani-Lenz syndactyly (CLS): review of the literature and attempt of classification.},
  author={Christoph Harpf and Marian Pavelka and Heribert Hussl},
  journal={British journal of plastic surgery},
  year={2005},
  volume={58 2},
  pages={251-7}
}
An oligodactylous variant of Cenani-Lenz syndactyly and its surgical treatment is presented. The deformity is believed to be of autosomal recessive inheritance and caused by a disordered axial and longitudinal differentiation of the upper and lower extremities. The classical form is mainly characterised by a complete syndactyly of the hands. Malformations may also affect the bones of the forearm and, to a lesser extent, the lower limbs. We analysed clinical features and compared them with those… CONTINUE READING