A peri-trigonal giant tumefactive cavernous malformation: case report and review of literature


Giant cavernous malformations (GCMs) constitute an uncommon entity in the diagnostic armamentarium of the neurosurgeon. We report a 3-year-old boy with a GCM in the peri-trigonal region and review 13 other paediatric cases previously reported in literature. A 3-year-old boy presented with right-sided hemiparesis and features of raised intracranial pressure of short duration. Computed tomography showed a large left peri-trigonal mass with a bleed. Magnetic resonance imaging showed associated perilesional edema and mass effect, rendering the lesion a tumefactive appearance. He underwent total excision of the lesion, with subsequent recovery of hemiparesis. Histopathology was reported as a cavernoma. The clinico-radiological presentation of GCM is discussed based on a case report and relevant cases in literature. Good surgical outcome can be expected with total microsurgical excision. A giant cavernous malformation should be one of the differentials of a lesion with a tumefactive clinico-radiological presentation in children. There should be a high index of suspicion for such a diagnosis, especially when the lesion does not enhance with contrast. This is the third case report in paediatric literature describing a periventricular location of this unusual lesion.

DOI: 10.1007/s00381-010-1237-4

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@article{Thakar2010APG, title={A peri-trigonal giant tumefactive cavernous malformation: case report and review of literature}, author={Sumit Thakar and Sunil Valentine Furtado and Nandita Ghosal and Alangar Sathya Hegde}, journal={Child's Nervous System}, year={2010}, volume={26}, pages={1819-1823} }