A new form of herniation: the Chiari V malformation

@article{Tubbs2011ANF,
  title={A new form of herniation: the Chiari V malformation},
  author={R. Shane Tubbs and Mitchel A. Muhleman and Marios Loukas and Walter Jerry Oakes},
  journal={Child's Nervous System},
  year={2011},
  volume={28},
  pages={305-307}
}
The Chiari malformations (CM) were first described by Hans Chiari roughly a century ago. Most of these malformations result in herniation of part of the cerebellum and brain stem into and through the foramen magnum. This herniation may cause impingement on the structures in the foramen magnum and upper part of the spinal canal with possible blockage of cerebral spinal fluid. Symptoms may include headache, neck pain, numbness of the extremities, dysphagia, nausea, and vomiting. Often the… 

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References

SHOWING 1-10 OF 16 REFERENCES
Vanishing cerebellum in myelomeningocoele.
TLDR
It is suggested that posterior fossa changes in myelomeningocoele are secondary results of prolonged prenatal spinal cerebrospinal fluid leak, which results in 'degeneration' of cerebellar tissue, presumably due to mechanically induced ischaemia.
Cerebellar agenesis versus vanishing cerebellum in Chiari II malformation.
  • R. Sener
  • Medicine
    Computerized medical imaging and graphics : the official journal of the Computerized Medical Imaging Society
  • 1995
Rhombencephalosynapsis and a Chiari II malformation.
TLDR
It is suggested that rhombencephalosynapsis can be associated with spinal malformations and, furthermore, that cases with the common features of rhombENCEphalosyapsis and a Chiari II malformation can exist.
Imaging diagnosis--cerebellar displacement and spina bifida in a calf.
  • S. Testoni, A. Dalla Pria, A. Gentile
  • Medicine
    Veterinary radiology & ultrasound : the official journal of the American College of Veterinary Radiology and the International Veterinary Radiology Association
  • 2010
TLDR
A calf affected by cerebellar displacement and spina bifida, diagnosed by ultrasonography, is described, which resembles the Arnold-Chiari malformation in humans.
Malformations of the Midbrain and Hindbrain: A Retrospective Study and Review of the Literature
TLDR
A retrospective analysis of radiological and clinical findings in 45 cases of midbrain–hindbrain anomalies finds integrated classification of malformations based on morphology, embryology and molecular neurogenetics may be useful.
Cerebellar Agenesis: Clinical, Neuropsychological and MR Findings
TLDR
No conclusion could be drawn whether impaired cognitive development and neuropsychological test performance were directly related to lack of cerebellar function, or caused by impaired motor development and performance.
Rhombencephalosynapsis: cerebellar embryogenesis.
TLDR
In an attempt to identify the pathogenesis of these anatomic manifestations of rhombencephalosynapsis, the traditional concept of the embryologic development of the cerebellar primordium is questioned.
Cerebellar agenesis.
  • M. Glickstein
  • Medicine, Psychology
    Brain : a journal of neurology
  • 1994
TLDR
Evidence is presented that it is this case which gave rise to part of the oral tradition which alleges that normal movement is possible despite total cerebellar agenesis, and despite an oral tradition to the contrary, there is absolutely no evidence about the motor capacities of this man during his life.
Dexterity in cerebellar agenesis
Arnold Chiari malformation type 0 Chiari 0 patients with Chiari I symptoms
  • General Medicine by Suite 101, http://www.suite101.com/content/arnold-chiari-malformation-doessize-matter-a136238. Accessed
  • 2009
...
1
2
...