A nationwide study of acquired C1-inhibitor deficiency in France

@inproceedings{Gobert2016ANS,
  title={A nationwide study of acquired C1-inhibitor deficiency in France},
  author={Delphine Gobert and Romain Paule and Denise Ponard and Pierre P. L{\'e}vy and V{\'e}ronique Fr{\'e}meaux-Bacchi and Laurence Bouillet and Isabelle Boccon-Gibod and Christian Drouet and St{\'e}phane Gayet and David Launay and Ludovic Martin and Ars{\`e}ne M{\'e}kinian and V{\'e}ronique Leblond and Olivier Fain},
  booktitle={Medicine},
  year={2016}
}
Acquired angioedema (AAE) due to C1-inhibitor (C1INH) deficiency is rare. Treatment options for acute attacks are variable and used off-label. Successful treatment of the associated lymphoma with rituximab seems to prevent acute attacks in subjects with AAE. The aim of this study was to describe AAE manifestations, its associated diseases, and patients' responses to treatments in a representative cohort.A retrospective nationwide study was conducted in France. The inclusion criteria were… CONTINUE READING
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