A nationwide study of acquired C1-inhibitor deficiency in France

  title={A nationwide study of acquired C1-inhibitor deficiency in France},
  author={Delphine Gobert and Romain Paule and Denise Ponard and Pierre P. L{\'e}vy and V{\'e}ronique Fr{\'e}meaux-Bacchi and Laurence Bouillet and Isabelle Boccon-Gibod and Christian Drouet and St{\'e}phane Gayet and David Launay and Ludovic Martin and Ars{\`e}ne M{\'e}kinian and V{\'e}ronique Leblond and Olivier Fain},
Acquired angioedema (AAE) due to C1-inhibitor (C1INH) deficiency is rare. Treatment options for acute attacks are variable and used off-label. Successful treatment of the associated lymphoma with rituximab seems to prevent acute attacks in subjects with AAE. The aim of this study was to describe AAE manifestations, its associated diseases, and patients' responses to treatments in a representative cohort.A retrospective nationwide study was conducted in France. The inclusion criteria were… CONTINUE READING
7 Citations
42 References
Similar Papers


Publications citing this paper.
Showing 1-7 of 7 extracted citations


Publications referenced by this paper.
Showing 1-10 of 42 references

High prevalence of splenic marginal zone lymphoma among patients with acquired C 1 inhibitor de fi ciency

  • WuMA Castelli R, ArquatiM
  • Br J Haematol
  • 2016

Acquired C 1 esterase inhibitor de fi ciency in a marginal zone lymphoma patient treated with rituximab

  • O Ates, V Sunar, T Babacan
  • J BUON
  • 2015

Bene fi ts of hydroxychloroquine in the treatment of a patient with angioedema due to acquired C 1 inhibitor de fi ciency

  • D Vincent, D Ponard, S Fiorella
  • Ann Allergy Asthma Immunol
  • 2015

Similar Papers

Loading similar papers…