A hypocomplementemic vasculitic urticarial syndrome. Report of four new cases and definition of the disease.

@article{Zeiss1980AHV,
  title={A hypocomplementemic vasculitic urticarial syndrome. Report of four new cases and definition of the disease.},
  author={C. Raymond Zeiss and Francis X. Burch and Robert Joel Marder and Nancy L. Furey and Frank R. Schmid and Henry Gewurz},
  journal={The American journal of medicine},
  year={1980},
  volume={68 6},
  pages={
          867-75
        }
}
We describe four new patients with a unique syndrome of persistent urticaria, with leukoclastic angiitis, severe angioedema, occasional life-threatening laryngeal edema, arthritis, arthralgia, neurologic abnormalities and pronounced persistent hypocomplementemia. The complement abnormalities involved markedly reduced levels of the Clq subunit of the first component of complement (Cl) in the presence of near normal levels of Clr and Cls subunits of Cl; modest to marked depletion of the fourth… CONTINUE READING

Citations

Publications citing this paper.
SHOWING 1-10 OF 11 CITATIONS

[The situation regarding hypocomplementemic urticarial vasculitis in 2015].

  • Annales de dermatologie et de venereologie
  • 2015
VIEW 6 EXCERPTS
HIGHLY INFLUENCED

Vasculitis of the mesenteric circulation.

  • Best practice & research. Clinical gastroenterology
  • 2017
VIEW 1 EXCERPT
CITES BACKGROUND