A case with pachyonychia congenita and B-cell lymphoma.

  title={A case with pachyonychia congenita and B-cell lymphoma.},
  author={Vitorino Modesto dos Santos and Thiago Pereira Loures and Jo{\~a}o Daniel Bringel Rego and Christiane Aires Teixeira and Kayursula Dantas de Carvalho and Afonso Lucas Oliveira Nascimento},
  journal={Acta medica Iranica},
  volume={52 7},
Pachyonychia congenital (PC) is a rare autosomal dominant genodermatosis characterized hyperkeratosis affecting the nails and palmoplantar areas, oral leukokeratosis, and cystic lesions. A 39-year-old woman with PC type 1 (Jadassohn-Lewandowsky syndrome) and B-cell lymphoma is described. No similar disorders or parental consanguinity were found in her family. Typical features of PC developed since her early childhood and the diagnosis of B-cell lymphoma was established seven years ago, without… CONTINUE READING