A case of adams-oliver syndrome.

  title={A case of adams-oliver syndrome.},
  author={Jong-Keun Seo and Ju-Hyun Kang and Hyun-Jae Lee and Deborah Lee and Ho Suk Sung and Seon-Wook Hwang},
  journal={Annals of dermatology},
  volume={22 1},
Adams-Oliver syndrome (AOS) is a congenital condition characterized by aplasia cutis congenita, transverse limb defects, and cutis marmorata telangiectatica. AOS can also be associated with extensive lethal anomalies of internal organs, including the central nervous, cardiopulmonary, gastrourointestinal, and genitourinary systems. Generally, the more severe these interrelated anomalies are, the poorer the prognosis becomes. In the relevant literature on this topic, it is somewhat unclear as to… 

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  • R. BeckerJ. Kunze N. Sarioglu
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    Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and Gynecology
  • 2002
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