A Systematic Review and Meta-analysis on the Epidemiology of the Muscular Dystrophies

  title={A Systematic Review and Meta-analysis on the Epidemiology of the Muscular Dystrophies},
  author={Jean K. Mah and Lawrence Korngut and Kirsten M. Fiest and Jonathan Dykeman and Lundy Day and Tamara Pringsheim and Nathalie Jett{\'e}},
  journal={Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques},
  pages={163 - 177}
  • J. Mah, L. Korngut, N. Jetté
  • Published 24 November 2015
  • Medicine
  • Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques
Abstract Background: The muscular dystrophies are a heterogeneous group of genetic muscle diseases with variable distribution of weakness and mode of inheritance. Methods: We previously performed a systematic review of worldwide population-based studies on Duchenne and Becker muscular dystrophies; the current study focused on the epidemiology of other muscular dystrophies using Medline and EMBASE databases. Two reviewers independently reviewed all abstracts, full-text articles, and abstracted… 
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