A Multidimensional Index and Staging System for Idiopathic Pulmonary Fibrosis

@article{Ley2012AMI,
  title={A Multidimensional Index and Staging System for Idiopathic Pulmonary Fibrosis},
  author={Brett Ley and Christopher J. Ryerson and Eric Vittinghoff and Jay H Ryu and Sara Tomassetti and Joyce S Lee and Venerino Poletti and Matteo Buccioli and Brett M Elicker and Kirk D Jones and Talmadge E. King and Harold R. Collard},
  journal={Annals of Internal Medicine},
  year={2012},
  volume={156},
  pages={684 - 691}
}
BACKGROUND Idiopathic pulmonary fibrosis (IPF) is a progressive fibrotic lung disease with an overall poor prognosis. A simple-to-use staging system for IPF may improve prognostication, help guide management, and facilitate research. OBJECTIVE To develop a multidimensional prognostic staging system for IPF by using commonly measured clinical and physiologic variables. DESIGN A clinical prediction model was developed and validated by using retrospective data from 3 large, geographically… Expand
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