• Corpus ID: 1254785

A Different Presentation of Mal De Meleda: New Skin Lesions in a Residual Limb after Traumatic Amputation.

@article{Adgzel2016ADP,
  title={A Different Presentation of Mal De Meleda: New Skin Lesions in a Residual Limb after Traumatic Amputation.},
  author={Emre Adıg{\"u}zel and Emine Y{\"u}ksel and Ismail Safaz and Arif Kenan Tan},
  journal={Acta dermatovenerologica Croatica : ADC},
  year={2016},
  volume={24 2},
  pages={
          137-9
        }
}
Mal de Meleda is a rare autosomal recessive skin disease which is known as keratoderma palmoplantaris transgradiens. Here we report a case of Mal de Meleda who had skin lesions in the residual limb and pseudoainhum in the thigh after traumatic lower leg amputation. A 71-year-old female was admitted to our tertiary hospital for prosthetic rehabilitation. On the physical examination, thickening of the skin on palms, left sole and residual limb was present. The patient reported that she had these… 

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References

SHOWING 1-10 OF 17 REFERENCES
Mal de Meleda with Lip Involvement: A Report of Two Cases
TLDR
Two patients with rare autosomal recessive transgradient palmoplantar keratoderma with unusual lip involvement are presented, without any family history.
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TLDR
An atypical case of full trisomy 13 in an infant who developed generalized milia without resolution is reported, and the patient died of heart failure at 10 months of age.
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TLDR
A bilateral pseudoainhum of all fingers in a 64-year-old fair-skinned woman with breast cancer, systemic scleroderma, and primary biliary cirrhosis with antimitochondrial antibodies M2 is reported.
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TLDR
A historical review of the literature data throughout the centuries till today of Mal de Meleda disease, an indigenous dermatological disease classified as a hereditary palmoplantar keratoderma, which entered the international scientific literature under that very name and has preserved it until today.
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TLDR
The relationship between the patients in Meleda and those in Anatolia awaits discovery by further researches that will be carried out with the collaboration of dermatology, genetics and medical history departments.
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TLDR
In this review, the current understanding, diagnostic criteria, and management of pseudo‐ainhum are discussed and the nomenclature of pseudo‑ainhum is clarified to allow for more efficient exploration of pseudo-ainhum, its causes, and therapeutic approaches.
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TLDR
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TLDR
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TLDR
A patient is described in whom continuous manipulation of the hair resulted in both a constricting band of hair around one finger and the unusual hair formation known as plica neuropathica, which was near amputation of the finger.
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