327 Hypogonadotropic Hypogonadism (hhg) in Acute Intermit Tent Porphyria (aip)


HHG in AIP has not been reported. A 20 yr. old male with AIP and inappropriate secretion of ADH was hyposmic, tall (178 cm), eunuchoid (U/L, 0.84), had a high-pitched voice, absent facial hair and Tanner 2-3 pubic hair. His testes were small (R, 8 ml; L, 10 ml). Karyotype was XY. Basal serum FSH, 5.5 mIU/ml; LH, 5.6 mIU/ml and T, 54 ng/dl were all low and… (More)
DOI: 10.1203/00006450-197804001-00332


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