β-Mannosidase in human leukocytes and fibroblasts

Abstract

In human leukocytes and fibroblasts β-mannosidase activity has a unimodal pH optimum (4.0–4.5). Markedly reduced activity is found in I-cell disease. Normal activities in human fibroblasts are ten times higher than in the goat, in which species a deficiency disease has been described. 
DOI: 10.1007/BF01805598

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Cite this paper

@article{Panday2005MannosidaseIH, title={β-Mannosidase in human leukocytes and fibroblasts}, author={Regeant Panday and Otto P. van Diggelen and Willem J. Kleijer and Martinus F. Niermeijer}, journal={Journal of Inherited Metabolic Disease}, year={2005}, volume={7}, pages={155-156} }