[Supravalvular aortic stenosis syndrome with advanced mitral regurgitation requiring extended aortoplasty and mitral valve replacement: a case report].

@article{Noguchi1991SupravalvularAS,
  title={[Supravalvular aortic stenosis syndrome with advanced mitral regurgitation requiring extended aortoplasty and mitral valve replacement: a case report].},
  author={Kyo Noguchi and Kenichi Sudo and Hideki Morita and Hiroyuki Yanagisawa and Tokuji Unno and Noriyuki Hayashi and Mamoru Tadokoro and J Kokubo and Kazuyuki Ikeda and Akihiro Mizuno},
  journal={Kyobu geka. The Japanese journal of thoracic surgery},
  year={1991},
  volume={44 4},
  pages={351-4}
}
This is a case report of a 28-year-old male, suffering from supravalvular aortic stenosis (systolic pressure gradient 60 mmHg) and severe mitral regurgitation associated with elfin face and mental retardation. Severely prolapsed mitral valve with elongated chordae tendineae was replaced with Björk-Shiley mitral valve prosthesis. Simultaneously, extended… CONTINUE READING