[Natural history of cavernomas of the central nervous system].

  title={[Natural history of cavernomas of the central nervous system].},
  author={Jacques Brunon and Christophe Nuti},
  volume={53 2-3 Pt 2},
We present a critical review of the literature on the central nervous system cavernomas in order to highlight their natural history and to define the most appropriate management of these rare lesions. The prevalence is now estimated from 0.3 to 0.7% in the general population without any significant difference by gender; 25% of cases are pediatric. Two forms of the disease can be described: sporadic forms in 80% of cases, characterized by isolated or rare lesions and familial dominant autosomic… CONTINUE READING