[Infantile genetic agranulocytosis (Kostmann syndrome)].

  • Helfried Gröbe
  • Published 1983 in
    Monatsschrift Kinderheilkunde : Organ der…


Infantile genetic agranulocytosis is characterized by recurrent infections usually leading to death in infancy or early childhood. Besides the severe neutropenia it shows variable monocytosis and hypergammaglobulinemia in the peripheral blood, and a maturation arrest at the promyelocyte-myelocyte level in the bone marrow. Consanguinity in some families, and… (More)


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