[Immunopathogenesis of idiopathic pulmonary fibrosis].

  title={[Immunopathogenesis of idiopathic pulmonary fibrosis].},
  author={Urszula Demkow},
  journal={Pneumonologia i alergologia polska},
  volume={82 1},
The paper presents the state of the art in the pathogenesis of idiopathic pulmonary fibrosis (IPF). Both, etiology and pathogenesis of IPF are unclear. The key elements in the pathogenesis of the disease are epithelial destruction and dysregulation of the phenotype of lung fibroblasts. Currently accepted hypothesis claims that IPF is not related to underlying inflammatory state but it is rather a result of pathological interaction between pulmonary epithelium and mesenchyme followed by… CONTINUE READING