• Publications
  • Influence
Food acceptance and neophobia in children with phenylketonuria: a prospective controlled study.
BACKGROUND In phenylketonuria (PKU), little is known about the effect of bitter-tasting phenylalanine-free l-amino acid exposure on taste preference development. The present prospective study aimedExpand
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The Micronutrient Status of Patients with Phenylketonuria on Dietary Treatment: An Ongoing Challenge
Background: In phenylketonuria (PKU), phenylalanine-free L-amino acid supplements are the major source of dietary micronutrients. Methods: Four hundred fifty-two retrospective annual/bi-annualExpand
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Home enteral feeding audit.
OBJECTIVE To determine the main problems that families experience in the first month after their child is discharged from hospital on home enteral tube feeds (HETF) in terms of obtaining feed andExpand
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Randomized comparison of a nutrient-dense formula with an energy-supplemented formula for infants with faltering growth.
INTRODUCTION The practice of supplementing standard infant formula with energy for infants with faltering growth has been widespread. This increases energy density but disturbs the protein : energyExpand
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Home enteral tube feeding in patients with inherited metabolic disorders: safety issues.
BACKGROUND Many children with inherited metabolic disorders (IMD), at risk of hypoglycaemia and metabolic decompensation, are dependent on long-term home overnight enteral tube feeding but its safetyExpand
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Home enteral tube feeding in children with inherited metabolic disorders: a review of long-term carer knowledge and technique.
BACKGROUND Home enteral tube feeding (HETF) is commonly used in children with inherited metabolic disorders (IMD). It is unclear how caregiver knowledge and their safety in using tube feedingExpand
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Dietary management of urea cycle disorders: UK practice.
BACKGROUND There is no published data describing UK dietary management of urea cycle disorders (UCD). The present study describes dietary practices in UK inherited metabolic disorder (IMD) centres.Expand
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Fibre content of enteral feeds for the older child.
BACKGROUND There is currently a lack of clinical data on fibre requirements in UK children. Subsequently, the ideal fibre profile for enteral formulae designed to meet the requirements of olderExpand
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Home enteral feeding audit 1 year post-initiation.
UNLABELLED OBJECTIVE To determine the practical problems that families of children on home enteral tube feeds (HETF) experience in the first year post-hospital discharge. METHODS ThirtyExpand
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Home delivery of dietary products in inherited metabolic disorders reduces prescription and dispensing errors.
UNLABELLED In the UK, for patients with inherited metabolic disorders (IMD) the traditional system for acquiring essential dietary products [patient prompted prescriptions generated by a medicalExpand
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