Paula Campos Perim

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Takayasu's arteritis (TA) is a systemic vasculitis that affects mainly the aorta and its major branches. Despite being the third most frequent vasculitis in childhood, the occurrence of TA in the pediatric age group is scarce. We report three cases of TA in children, emphasizing signs and symptoms, angiographic alterations and therapeutics.
Results Eight patients (4 males) were evaluated, being diagnosed 2 mutations in the perforin gene (in 3 patients, including twins), 3 secondary to Chèdiak-Higashi syndrome, 1 associated to Epstein-Baar virus infection, 1 associated to Kawasaki syndrome, and another unknown cause. The median age at diagnosis was 29,5 months (from 2 months to 12 years). The(More)
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