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Early pulmonary vascular disease in preterm infants at risk for bronchopulmonary dysplasia.
RATIONALE Pulmonary hypertension (PH) is associated with poor outcomes among preterm infants with bronchopulmonary dysplasia (BPD), but whether early signs of pulmonary vascular disease areExpand
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Cystic Fibrosis Foundation practice guidelines for the management of infants with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome during the first two years of life and
Through early detection, newborn screening (NBS)(1) for cystic fibrosis (CF) offers the opportunity for early intervention and improved outcomes. NBS programs screen for hypertrypsinogenemia, andExpand
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Clinical Utility of Echocardiography for the Diagnosis and Management of Pulmonary Vascular Disease in Young Children With Chronic Lung Disease
OBJECTIVE. The goal was to determine the clinical utility of Doppler echocardiography in predicting the presence and severity of pulmonary hypertension in patients with chronic lung disease whoExpand
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Late diagnosis defines a unique population of long-term survivors of cystic fibrosis.
Although the median survival for patients with cystic fibrosis (CF) is 32.9 years, a small group of patients live much longer. We analyzed the genotype and phenotype of CF patients 40 years and olderExpand
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Complications associated with symptomatic diagnosis in infants with cystic fibrosis.
OBJECTIVE To determine the complication and hospitalization rates in children with cystic fibrosis (CF) by mode of diagnosis. STUDY DESIGN Newly diagnosed cases of CF were identified from theExpand
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Effects of long-term sildenafil treatment for pulmonary hypertension in infants with chronic lung disease.
OBJECTIVE To determine the clinical course and outcomes of infants with chronic lung disease (CLD) and pulmonary hypertension (PH) who received prolonged sildenafil therapy. STUDY DESIGN WeExpand
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Effects of gender and age at diagnosis on disease progression in long-term survivors of cystic fibrosis.
RATIONALE Long-term survivors of cystic fibrosis (CF) (age > 40 yr) are a growing population comprising both patients diagnosed with classic manifestations in childhood, and nonclassic phenotypesExpand
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Scope and impact of early and late preterm infants admitted to the PICU with respiratory illness.
OBJECTIVE To determine the clinical course and outcomes of children born early preterm (EPT, <32 weeks), late preterm (LPT, 32 to 35 weeks), and full term (FT, >or=36 weeks) who were subsequentlyExpand
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Genome-wide association meta-analysis identifies five modifier loci of lung disease severity in cystic fibrosis
The identification of small molecules that target specific CFTR variants has ushered in a new era of treatment for cystic fibrosis (CF), yet optimal, individualized treatment of CF will requireExpand
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Cord blood angiogenic progenitor cells are decreased in bronchopulmonary dysplasia
Bronchopulmonary dysplasia (BPD), the chronic lung disease of prematurity, is associated with impaired vascular and alveolar growth. Antenatal factors contribute to the risk for developing BPD byExpand
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