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Treatment of cystinosis with cysteamine.
C v s T I N 0 S I S is a recessively inherited metabolic disorder characterized by an accumulation of nonprotein cystine within the lysosomes. 1 ! n the juvenile nephropathic form, the diseaseExpand
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The resolution of urinary or serum proteins by chromatography on DEAE cellulose columns with particular reference to urinary proteins after thermal burns.
Serum proteins were separated into the usual electrophoretic fractions by the starch block technique. Each fraction was then examined by DEAE cellulose chromatography and by starch gel electrophore...
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Attempts at reduction of intracellular cystine in infantile cystinosis, has been reported previously in 3 patients using dithiothreitol (2 patients) or cysteamine (mercaptoethylamine) (1 patient). WeExpand
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