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Different neurological and physiological profiles in POEMS syndrome and chronic inflammatory demyelinating polyneuropathy
Background POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein and skin changes) syndrome, a rare cause of demyelinating neuropathy associated with multiorgan involvement, has beenExpand
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Altered axonal excitability properties in amyotrophic lateral sclerosis: impaired potassium channel function related to disease stage.
Fasciculations are a characteristic feature of amyotrophic lateral sclerosis (ALS), and can arise proximally or distally in the motor neuron, indicating a widespread disturbance in membraneExpand
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Gangliosides contribute to stability of paranodal junctions and ion channel clusters in myelinated nerve fibers
Paranodal axo‐glial junctions are important for ion channel clustering and rapid action potential propagation in myelinated nerve fibers. Paranode formation depends on the cell adhesion moleculesExpand
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Differences in membrane properties of axonal and demyelinating Guillain‐Barré syndromes
Guillain‐Barré syndrome is classified into acute motor axonal neuropathy (AMAN) and acute inflammatory demyelinating polyneuropathy (AIDP) by electrodiagnostic and pathological criteria. In AMAN, theExpand
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Effect of localization of missense mutations in SCN1A on epilepsy phenotype severity
Background and Methods: Many missense mutations in the voltage-gated sodium channel subunit gene SCN1A were identified in patients with generalized epilepsy with febrile seizures plus (GEFS+) andExpand
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Utility of the distal compound muscle action potential duration for diagnosis of demyelinating neuropathies.
To assess the significance of distal compound muscle action potential (CMAP) duration for diagnosis of demyelinating neuropathies, electrophysiologic data were reviewed from 471 subjects, includingExpand
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Patterns of nerve conduction abnormalities in POEMS syndrome.
Polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes (POEMS) syndrome is a rare cause of demyelinating and axonal neuropathy. POEMS syndrome and chronic inflammatoryExpand
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Rho-kinase inhibition enhances axonal regeneration after peripheral nerve injury.
In injured adult neurons, the process of axonal regrowth and reestablishment of the neuronal function have to be activated. We assessed in this study whether RhoA, a key regulator of neuriteExpand
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Awaji ALS criteria increase the diagnostic sensitivity in patients with bulbar onset
OBJECTIVE To assess whether Awaji criteria improve the sensitivity of diagnosis for amyotrophic lateral sclerosis (ALS). In Awaji ALS criteria, fasciculation potentials are regarded as evidence ofExpand
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Selective block of calcium current by lanthanum in single bullfrog atrial cells
A single suction microelectrode voltage-clamp technique was used to study the actions of lanthanum ions (La3+) on ionic currents in single cells isolated from bullfrog right atrium. La3+, added asExpand
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