Two women (26 and 40 years old) developed an unusual microangiopathy that affected the brain and retina. Psychiatric symptoms initially overshadowed the subacute features of the progressive neurologic disorder. Ophthalmoscopic findings of multifocal branch retinal artery occlusions provided clinical evidence of vasculopathy. Laboratory data did not reveal… (More)
BACKGROUND Susac syndrome (SS) is a self-limited syndrome, presumably autoimmune, consisting of a clinical triad of encephalopathy, branch retinal artery occlusions, and hearing loss. All three elements of the triad may not be present or recognized, and MR imaging is often necessary to establish the diagnosis. OBJECTIVE To determine the spectrum of… (More)
In three patients, intractable hiccups occurred as part of the symptomatology of multiple sclerosis. In one patient intractable hiccups were the presenting complaint, and in another patient exacerbations of symptoms were almost always heralded by intractable hiccups. Intractable hiccups occur in a variety of diseases, including many that affect the… (More)
Three patients with inferior branch palsies of the oculomotor nerve are described. Two were under 10 years of age and the third was 30 years old at the onset. All 3 presented with painless diplopia. The onset was sudden in 2 patients and progressive in the third. The palsy cleared within a short time in the 2 patients with sudden onset, and a possible viral… (More)
Three patients presented with unilateral progressive optic neuropathy. None of these patients had signs of symptoms referable to the chiasm or eye, thus confining their decline in vision to the optic nerve. Clinical and neuroradiographic evidence suggested a meningioma involving the optic nerve at the orbital-canalicular junction in one patient and the… (More)
Computerized transaxial tomography is now the procedure of choice in diagnosing exophthalmos. Caution must be exercised, however, in interpreting the results. The patient reported here had a swollen inferior rectus muscle that simulated an orbital apex tumor on CAT scan.
We report two patients with optic disc drusen who suffered sudden, concentric constriction of the visual field. Visual acuity remained normal. The involved discs showed no swelling, hemorrhage, or other evidence of anterior ischemic optic neuropathy. We are unable to explain the mechanism or the pattern of visual field loss in these unusual cases.
A 38-year-old woman presented with a bilateral, chronic, progressive optic neuropathy following jejunoileal bypass surgery for morbid obesity. Standardized A-scan orbital echography revealed grossly swollen optic nerve sheaths with a positive 30 degrees test, indicating increased subarachnoid fluid. Review of reported complications of jejunoileal bypass… (More)
Experience in three cases has shown that a small meningioma in the extreme posterior portion of the orbit just anterior to the optic foramen may occur with progressive visual loss in the absence of orbital signs. Such lesions cannot be detected by plain skull roentgenography, polytomography, or selective angiography with subtraction and magnification. In… (More)