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Although there is evidence in experimental animals of the importance of the pedunculopontine area in locomotion, clinical lesion reports are lacking. An 83-year-old woman became unable to stand and to generate stepping movements after a hemorrhage at the pontomesencephalic junction involving the right pedunculopontine area. Her deficit resembled the gait(More)
Two siblings with proximal myotonic myopathy (PROMM), a hereditary disorder, had predominantly proximal weakness, pain, and gait impairment aggravated by warm temperatures. EMG of the deltoid showed sparse abnormal spontaneous activity at room temperature and with cooling. Warming induced frequent myotonic discharges and fibrillations. Profuse myotonia(More)
Orthostatic tremor (OT) is a clinically defined syndrome of leg tremor while standing. Controversy surrounds whether OT is a distinct syndrome or is an essential tremor (ET) variant. We report two patients with OT. Electrophysiological testing included polymyography, accelerometry, nerve conduction, and evoked potential studies. The effects of various(More)
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