Coexistence of hereditary coproporphyria with acute intermittent porphyria.
The results obtained suggest that deficiency of porphobilinogen deaminase and coproporphyrinogen oxidase can be inherited independently.
Porphyric polyneuropathy and its pathogenesis in the light of electrophysiological investigations
[Evaluation of porphyrogenic action of selected drugs].
Abnormalities in liver function and morphology and impaired aminopyrine metabolism in hereditary hepatic porphyrias.
Increased activity of porphobilinogen deaminase in erythrocytes during attacks of acute intermittent porphyria.
It was found that in most cases the activity of porphobilinogen deaminase was higher than 24.3 nmoles/ml erythrocytes/hour, a value considered as characteristic for acute intermittent porphyria, and that it decreased during convalescence and remission.
Ketamine in acute intermittent porphyria--dangerous or safe?
The function and morphology of the liver in porphyria cutanea tarda.
- J. Ostrowski, T. Michalak, B. Zawirska, E. Kostrzewska, M. Błaszczyk, A. Gregor
- MedicineAnnals of clinical research
The aminopyrine breath test, postprandial serum bile acids, and routine liver tests were assessed as indicators of liver dysfunction in 38 patients with porphyria cutanea tarda and there was no evident relationship between morphological and functional liver changes.
Heme arginate (Normosang) in the treatment of attacks of acute hepatic porphyrias.
- E. Kostrzewska, A. Gregor, S. Tarczyńska-Nosal
- MedicineMateria medica Polona. Polish journal of medicine…
- 1 October 1991
The treatment with heme arginate of 47 attacks of acute hepatic porphyrias are presented. Distribution of patients into three groups of severity has shown that the best clinical response is obtained…
Determination of serum proteins in the presence of dextran by means of the biuret reaction.
- A. Gregor, E. Kostrzewska, W. Godorowska
- ChemistryInfusionstherapie und klinische Ernährung
- 1 February 1977
264 biuret reagents for total protein determination in serum containing dextran were investigated. The usefulness of the method is dependent on proper ratio of the components of the reagent:…
Increased protoporphyrin in erythrocytes in a child with acute intermittent porphyria.
- A. Gregor, E. Kostrzewska, H. Prokurat, Z. Pucek, E. Torbicka
- MedicineArchives of disease in childhood
- 1 December 1977
A child is described with acute intermittent porphyria but having an erythropoietic component, with disordered metabolism of porphyrins in bone marrow.